Haemophilia inherited bleeding disorder: Dr Zahid

Karachi: Secretary Sindh Blood Transfusion Authority (SBTA) Dr Zahid Hasan Ansari said on Thursday Haemophilia is an inherited bleeding disorder that prevents blood from dotting properly.

Talking to PPI in connection with World Haemophilia Day 2014, Dr Zahid said haemophilia is a deficiency of a clotting factor in the blood that causes a person to bleed uncontrollably from mild injuries. He said a person with haemophilia does not bleed faster than anyone else, but bleeding may last longer. He said bleeding into joints and muscles can cause stiffness, pain, severe joint damage, disability, and sometimes death.

This year World Haemophilia Day will focus on encouraging the global bleeding disorders community to speak out and create change.

He informed that symptoms of haemophilia are big bruises, bleeding into muscles and joints, especially the knees, elbows, and ankles, sudden bleeding inside the body for no clear reason, prolonged bleeding after a cut, tooth removal, surgery, or an accident and serious internal bleeding into vital organs, most commonly after a serious trauma.

Dr Zahid said effective treatment for haemophilia is available, but as yet there is no cure. He said with proper treatment, people with haemophilia live relatively normal lives. He said there are several different types of haemophilia but the following two are the most common Haemophilia A and Haemophilia B (Christmas Disease).

He said universal incidence of haemophilia is about 1 in 5,000 – 10,000 male births. He informed that there is no specific data available in Pakistan about the haemophilia disease. He said males are affected and females carriers of this disease. He said patients are suffering from disease should avoid aspirin and intra muscular injections during complication.

According to Pakistan Haemophilia Patients Welfare Society (PHPWS), data available estimated 400,000 people worldwide (9000 people in Pakistan) were suffering this disease.

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